Issue Information ‐ TOC
Liver Transplantation2016Vol. 22(9), pp. 1178–1180
Garrett R. Roll, Peter G. Stock, Bruno Roche, Didier Samuel, Juan J. Araiz, Trinidad Serrano, Francisco Garc Ia-Gil, Elena Lacruz, Sara Lorente, I Anchez, Miguel Suarez, Joseph R. Scalea, Robert R. Redfield, David P. Foley, Ilaria Lenci, Leonardo Baiocchi, Laura Tariciotti, Daniele Di Paolo, Martina Milana, Francesco Santopaolo, Maria Tommaso, Luca Manzia, Valentina Toti, Giuseppe Svicher, Carlo Tisone, Mario Perno, Fredric D. Gordon, David S. Goldberg, Nathan P. Goodrich, Anna S. Lok, Elizabeth C. Verna, Nazia Selzner, R. Todd Stravitz, Robert M. Merion, Dieter P. Hoyer, Andreas Paul, Sebastian Luer, Henning Reis, Patrik Efferz, Thomas Minor, Shinya Okumura, Takumi Teratani, Yasuhiro Fujimoto, Xiangdong Zhao, Tatsuaki Tsuruyama, Yuki Masano, Naoya Kasahara, Taku Iida, Shintaro Yagi, Tadahiro Uemura, Toshimi Kaido, Shinji Üemoto, Achiya Amir, Simon C. Ling, Ahmed Naqvi, Sheila Weitzman, Annie Fecteau, David Grant, Anand Ghanekar, Mark S. Cattral, Nadya Nalli, Ernest Cutz, Binita M. Kamath, Nicola L. Jones, Maria De Angelis, Vicky L. Ng, Yaron Avitzur, Paulo Lisboa Bittencourt, Alberto Queiróz Farias, Cláudia Alves Couto, Gloria de la Rosa, Constantino Fondevila, Miquel Navasa, Mohamed Rela, Ilankumaran Kaliamoorthy, Mettu Srinivas Reddy, Rodrigo Liberal, Diego Vergani, Giorgina Mieli‐Vergani, Jean-Bernard Otté, Adam Doyle, Oyedele Adeyi, Korosh Khalili, Sandra E. Fischer, Martín Dib, Nicolás Goldaracena, Jayne Dillon, Ian Mcgilvray, Paul D. Greig, Leslie Lilly, Eberhard L. Renner, Gary Levy, Michel Rayar, Giovanni Battista, Levi Sandri, Caterina Cusumano, Pauline Houssel‐Debry, Christophe Camus, Eronique Desfourneaux, M. Lakéhal, Bernard Meunier, Laurent Sulpice, Karim Boudjéma, Davide Reply, Paolo Ghinolfi, Daniele De Simone, Giulia Pezzati, Franco Cirillo, Franco Cirillo, Filipponi
Abstract
Acute liver failure due to secondary hemophagocytic lymphohistiocytosis (HLH) is a rare and life-threatening condition and is considered by many as a contraindication for liver transplantation. The diagnosis is challenging and based on the HLH-2004 criteria. Phagocytosed RBC in Kupffer cells can be seen on electron micrographs. Nine children underwent liver transplantation for this condition and received HLH-adjusted immunosuppressive treatment. Graft and patient survival were 60% and 67%, respectively. (Yaron Avitzur, M.D.)
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