Impaired cardiac and skeletal muscle bioenergetics in children, adolescents, and young adults with Barth syndrome
Physiological Reports2017Vol. 5(3)
Citations Over TimeTop 12% of 2017 papers
Adil Bashir, Kathryn L. Bohnert, Dominic N. Reeds, Linda R. Peterson, Adam J. Bittel, Lisa de las Fuentes, Christina A. Pacak, Barry J. Byrne, W. Todd Cade
Abstract
1.0 ± 0.2 mmol/L sec, P VO2peak but not resting cardiac function. Cardiac and skeletal muscle bioenergetics are impaired and appear to contribute to exercise intolerance in BTHS.
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