Hiroko Nikaido
Kanazawa University(JP)
Publications by Year
Research Areas
Metabolism and Genetic Disorders, Diet and metabolism studies, Mitochondrial Function and Pathology, Amino Acid Enzymes and Metabolism, Muscle metabolism and nutrition
Most-Cited Works
- → Primary systemic carnitine deficiency is caused by mutations in a gene encoding sodium ion-dependent carnitine transporter(1999)557 cited
- → Molecular and Physiological Evidence for Multifunctionality of Carnitine/Organic Cation Transporter OCTN2(2001)182 cited
- → Functional relevance of carnitine transporter OCTN2 to brain distribution ofl‐carnitine and acetyl‐l‐carnitine across the blood–brain barrier(2001)167 cited
- → Primary defect of juvenile visceral steatosis (jvs) mouse with systemic carnitine deficiency is probably in renal carnitine transport system(1994)85 cited
- → Carnitine administration to juvenile visceral steatosis mice corrects the suppressed expression of urea cycle enzymes by normalizing their transcription.(1992)78 cited
- → Cardiac hypertrophy in juvenile visceral steatosis (jvs) mice with systemic carnitine deficiency(1993)77 cited
- → Acetyl‐L‐carnitine permeability across the blood–brain barrier and involvement of carnitine transporter OCTN2(2003)76 cited
- → Decreased Tissue Distribution of l-Carnitine in Juvenile Visceral Steatosis Mice(1999)61 cited
- → Gene-Dose Effect on Carnitine Transport Activity in Embryonic Fibroblasts of JVS Mice as a Model of Human Carnitine Transporter Deficiency(1998)45 cited
- → Abnormal expression of urea cycle enzyme genes in juvenile visceral steatosis (jvs) mice(1992)41 cited