Maria Demestre
Institute for Bioengineering of Catalonia(ES)
Publications by Year
Research Areas
Amyotrophic Lateral Sclerosis Research, Neurogenetic and Muscular Disorders Research, Nerve injury and regeneration, Pluripotent Stem Cells Research, Neurofibromatosis and Schwannoma Cases
Most-Cited Works
- → 4-Aminopyridine Induced Activity Rescues Hypoexcitable Motor Neurons from Amyotrophic Lateral Sclerosis Patient-Derived Induced Pluripotent Stem Cells(2016)132 cited
- → FUS-mediated regulation of acetylcholine receptor transcription at neuromuscular junctions is compromised in amyotrophic lateral sclerosis(2019)126 cited
- → Intranasal Delivery of Neural Stem/Progenitor Cells: A Noninvasive Passage to Target Intracerebral Glioma(2012)101 cited
- → Formation and characterisation of neuromuscular junctions between hiPSC derived motoneurons and myotubes(2015)93 cited
- → CAPE (caffeic acid phenethyl ester)‐based propolis extract (Bio 30) suppresses the growth of human neurofibromatosis (NF) tumor xenografts in mice(2008)93 cited
- → NEK1 loss-of-function mutation induces DNA damage accumulation in ALS patient-derived motoneurons(2018)92 cited
- → Stimulated release of lactate in freely moving rats is dependent on the uptake of glutamate.(1997)87 cited
- → Super-Resolution Microscopy Reveals Presynaptic Localization of the ALS/FTD Related Protein FUS in Hippocampal Neurons(2016)81 cited
- → Autism-associated SHANK3 mutations impair maturation of neuromuscular junctions and striated muscles(2020)80 cited
- → FUS Mislocalization and Vulnerability to DNA Damage in ALS Patients Derived hiPSCs and Aging Motoneurons(2016)78 cited