J.L. Chuang
University of California, Berkeley(US)
Publications by Year
Research Areas
Biochemical Acid Research Studies, Metabolism and Genetic Disorders, Enzyme Structure and Function, Amino Acid Enzymes and Metabolism, Cancer, Hypoxia, and Metabolism
Most-Cited Works
- → The P7C3 class of neuroprotective compounds exerts antidepressant efficacy in mice by increasing hippocampal neurogenesis(2014)157 cited
- → Molecular Phenotypes in Cultured Maple Syrup Urine Disease Cells(1989)68 cited
- → Isolation and sequencing of a cDNA encoding the decarboxylase (E1)alpha precursor of bovine branched-chain alpha-keto acid dehydrogenase complex. Expression of E1 alpha mRNA and subunit in maple-syrup-urine-disease and 3T3-L1 cells.(1988)46 cited
- → Maple syrup urine disease in Mennonites. Evidence that the Y393N mutation in E1 alpha impedes assembly of the E1 component of branched-chain alpha-keto acid dehydrogenase complex.(1991)43 cited
- → Reactive oxygen species control protein degradation at the mitochondrial import gate(2024)35 cited
- → Cloning and expression in Escherichia coli of mature E1 beta subunit of bovine mitochondrial branched-chain alpha-keto acid dehydrogenase complex. Mapping of the E1 beta-binding region on E2.(1992)34 cited
- → Molecular and biochemical basis of intermediate maple syrup urine disease. Occurrence of homozygous G245R and F364C mutations at the E1 alpha locus of Hispanic-Mexican patients.(1995)34 cited
- → Structure of the gene encoding dihydrolipoyl transacylase (E2) component of human branched chain alpha-keto acid dehydrogenase complex and characterization of an E2 pseudogene.(1992)28 cited
- → E2 transacylase-deficient (type II) maple syrup urine disease. Aberrant splicing of E2 mRNA caused by internal intronic deletions and association with thiamine-responsive phenotype.(1997)25 cited
- → Production of Recombinant Mammalian Holo-E2 and E3 and Reconstitution of Functional Branched-Chain α-Keto Acid Dehydrogenase Complex with Recombinant E1(2000)25 cited